August 28, 2013: Hutchinson-Gilford Progeria Syndrome is an extremely rare genetic disease wherein symptoms resembling aspects of aging are manifested at a very early age. The word progeria comes from the Greek words "pro" (πρό), meaning "before" or "premature", and "gēras" (γῆρας), meaning "old age". The disorder has a very low incident rate, occurring in an estimated 1 per 8 million live births.
This is a condition known as Hutchinson-Gilford Progeria Syndrome. It is a very rare condition that accelerates the aging process in children. The average life span for children with this disorder is 13 years of age.
Progeria (also known as “Hutchinson–Gilford progeria syndrome” and “Hutchinson–Gilford syndrome”) is an extremely rare, severe, genetic condition wherein symptoms resembling aspects of aging are manifested at an early age.
Children who suffer from Hutchinson-Gilford Progeria syndrome age prematurely due to a defective protein in their cells. Scientists have now identified another important pathological factor: the system responsible for removing cellular debris and for breaking down defective proteins operates at lower levels in HGPS cells than in normal cells. The researchers have succeeded in reactivating protein breakdown in HGPS cells and thus reducing disease-related defects by using a substance from ...
The Progeria Research Foundation. Hutchinson-Gilford Progeria Syndrome ("Progeria", or "HGPS") is a rare, fatal genetic condition characterized by an appearance of accelerated aging in children. Its name is derived from the Greek and means "prematurely old." These children have the absolute biggest hearts in the world and are so wise for their young age. The age rapidly, many dying of heart attacks and strokes before age 15.